The 'Act on PAH Right Ventricle (RV) Masterclass in PAH and Adult Congenital Heart Disease (ACHD)' was attended by more than 90 people from the UK and Ireland on 13th–14th July 2018.

The aim of this masterclass was to provide delegates with an in-depth understanding of the physiology of the RV in health and disease, with a focus on the acquisition and interpretation of echocardiographic information. Echocardiography is an important tool that can be used to assess the probability of pulmonary hypertension (PH), and it plays a key role in the decision to refer patients with suspected PH to a specialist centre.  Evidence suggests that early diagnosis and intervention can improve patient outcomes1-4, however almost half of patients wait over a year after first experiencing symptoms before receiving a diagnosis.5


The RV masterclass programme was developed in collaboration with an expert faculty of PH and ACHD specialists from the Royal Brompton Hospital in London. This was a multidisciplinary meeting attended by cardiologists, respiratory physicians, specialist nurses and cardiac physiologists involved in the diagnosis and clinical management of patients with PAH and ACHD. The varied and interactive programme combined lectures and workshops for all attendees on the first day, with a smaller group of 30 delegates then having the opportunity to attend echocardiography and cardiac morphology workshops at the Royal Brompton Hospital on the second day. 




The plenary lectures provided a detailed overview of the morphology and physiology of the normal RV, versus that of the RV in PH. A central theme to the morning sessions was discussion of protocols for echocardiographic imaging in different types of PH.


"We hope we have contributed to raising awareness of pulmonary hypertension in echo departments around England."

Dr. Konstantinos Dimopoulos, Co-chair, Royal Brompton Hospital, London


Delegates chose to attend one of two parallel workshops during the afternoon. The specialist ACHD workshop provided lectures and ample discussion on conditions that cause RV pressure or volume overload, and how to screen CHD patients for PH. The general session on PH included lectures for non-specialists in the audience on the challenges of identifying PH in their centres, and provided guidance on how to interpret echocardiograms and decide which patients to refer to specialist PH services. These were followed by interactive case-based discussions, including cases of idiopathic PAH, chronic thromboembolic PH, PAH associated with connective tissue disease, and PH with left heart disease.

88% of attendees rated the quality of education at this meeting as “excellent”.



“This was an excellent quality educational meeting with first class speakers covering PAH and ACHD. I would be keen to attend any further meetings. The topics today, discussions and case studies will definitely inform and impact on my practice”

Delegate feedback


For those who attended the Act on PAH RV Masterclass, thank you for contributing to this interactive event. We hope that the meeting has inspired you to take action and improve patient outcomes with earlier identification and referral of patients with suspected PH to a specialist centre.



  1. Humbert M, et al. Circulation 2010; 122:156–163
  2. Humbert M, et al. Eur Respir J 2010; 36:549–555
  3. Condliffe R, et al. Am J Respir Crit Care Med 2009;179:151–157
  4. Pulmonary Hypertension Association UK (2017). What it means to live with PH today. PHA UK. Available from: 
  5. Dimopoulos K, et al. Circulation 2010;121:20–25

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